Annotation Detail

Information
Associated Genes
PKHD1
Associated Variants
PKHD1 p.Ile3555Lys (p.I3555K) ( ENST00000371117.8 )
PKHD1 p.Ile3555Lys (p.I3555K) ( ENST00000371117.8 )
Associated Disease
not provided
Source Database
ClinVar
Description
NM_138694.4(PKHD1):c.10664T>A (p.Ile3555Lys) AND not provided
ClinVar Allele ID
195478
ClinVar RefSeq Alternation Syntax
NM_138694.4:c.10664T>A
Clinical Significance Description
Likely pathogenic
Clinical Significance Last Update
2015-05-14
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000179598
ClinVar Disease
not provided
Observed Origin Sample
germline
Drugs