Annotation Detail

Information
Associated Genes
GNPTAB
Associated Variants
GNPTAB p.Leu126Ter (p.L126*) ( ENST00000299314.12, ENST00000549940.5 )
GNPTAB p.Leu126Ter (p.L126*) ( ENST00000299314.12, ENST00000549940.5 )
Associated Disease
not provided
Source Database
ClinVar
Description
NM_024312.5(GNPTAB):c.377T>A (p.Leu126Ter) AND not provided
ClinVar Allele ID
195019
ClinVar RefSeq Alternation Syntax
NM_024312.5:c.377T>A
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2014-05-22
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000178995
ClinVar Disease
not provided
Observed Origin Sample
germline
Drugs