Annotation Detail

Information
Associated Genes
IDUA
Associated Variants
IDUA c.494-1G>C ( ENST00000247933.9, ENST00000514224.2 )
IDUA c.494-1G>C ( ENST00000247933.9, ENST00000514224.2 )
Associated Disease
not provided
Source Database
ClinVar
Description
NM_000203.5(IDUA):c.494-1G>C AND not provided
ClinVar Allele ID
194805
ClinVar RefSeq Alternation Syntax
NM_001363576.1:c.98-1G>C
ClinVar RefSeq Alternation Syntax
NM_000203.5:c.494-1G>C
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2015-06-01
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000178734
ClinVar Disease
not provided
Observed Origin Sample
germline
Drugs