Annotation Detail

Information
Associated Genes
OPA1
Associated Variants
OPA1 p.Glu724ThrfsTer7 (p.E724Tfs*7) ( ENST00000361150.6, ENST00000361510.8, ENST00000361715.6, ENST00000361828.7, ENST00000361908.8, ENST00000392436.7, ENST00000392437.6, ENST00000643329.1, ENST00000645553.1, ENST00000646793.1 )
OPA1 p.Glu724ThrfsTer7 (p.E724Tfs*7) ( ENST00000361150.6, ENST00000361510.8, ENST00000361715.6, ENST00000361828.7, ENST00000361908.8, ENST00000392436.7, ENST00000392437.6, ENST00000643329.1, ENST00000645553.1, ENST00000646793.1 )
Associated Disease
not provided
Source Database
ClinVar
Description
NM_130837.3(OPA1):c.2224_2225del (p.Glu742fs) AND not provided
ClinVar Allele ID
192776
ClinVar RefSeq Alternation Syntax
NM_130837.3:c.2224_2225del
ClinVar RefSeq Alternation Syntax
NM_130834.3:c.2113_2114del
ClinVar RefSeq Alternation Syntax
NM_015560.3:c.2059_2060del
ClinVar RefSeq Alternation Syntax
NM_130832.3:c.2005_2006del
ClinVar RefSeq Alternation Syntax
NM_130831.3:c.1951_1952del
ClinVar RefSeq Alternation Syntax
NM_130833.3:c.2062_2063del
ClinVar RefSeq Alternation Syntax
NM_130836.3:c.2170_2171del
ClinVar RefSeq Alternation Syntax
NM_001354664.2:c.1687_1688del
ClinVar RefSeq Alternation Syntax
NM_130835.3:c.2116_2117del
ClinVar RefSeq Alternation Syntax
NM_001354663.2:c.1690_1691del
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2015-01-07
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000176222
ClinVar Disease
not provided
Observed Origin Sample
germline
Drugs