Annotation Detail

Information
Associated Genes
SMPD1
Associated Variants
SMPD1 p.Ser192AlafsTer65 (p.S192Afs*65) ( ENST00000527275.5, ENST00000342245.9 )
SMPD1 p.Ser192AlafsTer65 (p.S192Afs*65) ( ENST00000342245.9, ENST00000527275.5 )
Associated Disease
not provided
Source Database
ClinVar
Description
NM_000543.5(SMPD1):c.573del (p.Ser192fs) AND not provided
ClinVar Allele ID
178086
ClinVar RefSeq Alternation Syntax
NM_000543.5:c.573del
ClinVar RefSeq Alternation Syntax
NM_001318087.2:c.573del
ClinVar RefSeq Alternation Syntax
NM_001318088.2:c.-389del
ClinVar RefSeq Alternation Syntax
NM_001007593.3:c.570del
ClinVar RefSeq Alternation Syntax
NM_001365135.2:c.573del
ClinVar RefSeq Alternation Syntax
NR_027400.3:n.698del
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2023-09-01
Clinical Significance Review Status
criteria provided, multiple submitters, no conflicts
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000175623
ClinVar Disease
not provided
Observed Origin Sample
germline
Drugs