Annotation Detail

Information
Associated Genes
OPA1
Associated Variants
OPA1 p.Leu488TrpfsTer16 (p.L488Wfs*16) ( ENST00000361150.6, ENST00000361510.8, ENST00000361715.6, ENST00000361828.7, ENST00000361908.8, ENST00000392436.7, ENST00000392437.6, ENST00000643329.1, ENST00000645553.1, ENST00000646793.1 )
OPA1 p.Leu488TrpfsTer16 (p.L488Wfs*16) ( ENST00000361150.6, ENST00000361510.8, ENST00000361715.6, ENST00000361828.7, ENST00000361908.8, ENST00000392436.7, ENST00000392437.6, ENST00000643329.1, ENST00000645553.1, ENST00000646793.1 )
Associated Disease
not provided
Source Database
ClinVar
Description
NM_130837.3(OPA1):c.1517del (p.Leu506fs) AND not provided
ClinVar Allele ID
101607
ClinVar RefSeq Alternation Syntax
NM_130837.3:c.1517del
ClinVar RefSeq Alternation Syntax
NM_130833.3:c.1355del
ClinVar RefSeq Alternation Syntax
NM_130836.3:c.1463del
ClinVar RefSeq Alternation Syntax
NM_130831.3:c.1244del
ClinVar RefSeq Alternation Syntax
NM_015560.3:c.1352del
ClinVar RefSeq Alternation Syntax
NM_001354663.2:c.983del
ClinVar RefSeq Alternation Syntax
NM_130832.3:c.1298del
ClinVar RefSeq Alternation Syntax
NM_001354664.2:c.980del
ClinVar RefSeq Alternation Syntax
NM_130835.3:c.1409del
ClinVar RefSeq Alternation Syntax
NM_130834.3:c.1406del
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2013-01-25
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000174779
ClinVar Disease
not provided
Observed Origin Sample
germline
Drugs