Annotation Detail

Information
Associated Genes
PAH
Associated Variants
PAH p.Phe55Leu (p.F55L) ( ENST00000307000.7, ENST00000553106.6 )
PAH p.Phe55Leu (p.F55L) ( ENST00000307000.7, ENST00000553106.6 )
Associated Disease
not provided
Source Database
ClinVar
Description
NM_000277.3(PAH):c.165T>G (p.Phe55Leu) AND not provided
ClinVar Allele ID
98641
ClinVar RefSeq Alternation Syntax
NM_000277.3:c.165T>G
ClinVar RefSeq Alternation Syntax
NM_001354304.2:c.165T>G
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2023-02-01
Clinical Significance Review Status
criteria provided, multiple submitters, no conflicts
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000078512
ClinVar Disease
not provided
Observed Origin Sample
germline
Observed Origin Sample
not provided
Drugs