Annotation Detail

Information
Associated Genes
RET
Associated Variants
RET p.Val804Met (p.V804M) ( ENST00000713926.1, ENST00000340058.6, ENST00000355710.8, ENST00000615310.5 )
RET p.Ser904Cys (p.S904C) ( ENST00000615310.5, ENST00000355710.8, ENST00000713926.1, ENST00000340058.6 )
RET p.Val804Met (p.V804M) ( ENST00000340058.6, ENST00000355710.8, ENST00000615310.5, ENST00000713926.1 )
RET p.Ser904Cys (p.S904C) ( ENST00000340058.6, ENST00000355710.8, ENST00000615310.5, ENST00000713926.1 )
Associated Disease
multiple endocrine neoplasia type 2B
Source Database
ClinVar
Description
NM_020975.4(RET):c.[2410G>A;2711C>G] AND Multiple endocrine neoplasia type 2B
ClinVar Allele ID
28984
ClinVar Allele ID
36303
ClinVar RefSeq Alternation Syntax
NM_001406773.1:c.2273C>G
ClinVar RefSeq Alternation Syntax
NM_001406770.1:c.2122G>A
ClinVar RefSeq Alternation Syntax
NM_001406771.1:c.2273C>G
ClinVar RefSeq Alternation Syntax
NM_001355216.2:c.1648G>A
ClinVar RefSeq Alternation Syntax
NM_001406788.1:c.1526C>G
ClinVar RefSeq Alternation Syntax
NM_001406791.1:c.1406C>G
ClinVar RefSeq Alternation Syntax
NM_020975.6:c.2410G>A
ClinVar RefSeq Alternation Syntax
NM_001406789.1:c.1526C>G
ClinVar RefSeq Alternation Syntax
NM_001406763.1:c.2275G>A
ClinVar RefSeq Alternation Syntax
NM_001406764.1:c.2582C>G
ClinVar RefSeq Alternation Syntax
NM_001406762.1:c.2582C>G
ClinVar RefSeq Alternation Syntax
NM_001406777.1:c.1684G>A
ClinVar RefSeq Alternation Syntax
NM_001406778.1:c.1684G>A
ClinVar RefSeq Alternation Syntax
NM_001406765.1:c.2576C>G
ClinVar RefSeq Alternation Syntax
NM_001406769.1:c.2014G>A
ClinVar RefSeq Alternation Syntax
NM_001406792.1:c.961G>A
ClinVar RefSeq Alternation Syntax
NM_001406759.1:c.2711C>G
ClinVar RefSeq Alternation Syntax
NM_001406761.1:c.2582C>G
ClinVar RefSeq Alternation Syntax
NM_001406780.1:c.1513G>A
ClinVar RefSeq Alternation Syntax
NM_001406772.1:c.2315C>G
ClinVar RefSeq Alternation Syntax
NM_020629.2:c.2410G>A
ClinVar RefSeq Alternation Syntax
NM_001406781.1:c.1513G>A
ClinVar RefSeq Alternation Syntax
NM_001406768.1:c.2146G>A
ClinVar RefSeq Alternation Syntax
NM_001406782.1:c.1513G>A
ClinVar RefSeq Alternation Syntax
NM_001406784.1:c.1721C>G
ClinVar RefSeq Alternation Syntax
NM_001406772.1:c.2014G>A
ClinVar RefSeq Alternation Syntax
NM_001406792.1:c.1262C>G
ClinVar RefSeq Alternation Syntax
NM_020975.6:c.2711C>G
ClinVar RefSeq Alternation Syntax
NM_001406780.1:c.1814C>G
ClinVar RefSeq Alternation Syntax
NM_001406793.1:c.1262C>G
ClinVar RefSeq Alternation Syntax
NM_001406788.1:c.1225G>A
ClinVar RefSeq Alternation Syntax
NM_001406773.1:c.1972G>A
ClinVar RefSeq Alternation Syntax
NM_001406774.1:c.2186C>G
ClinVar RefSeq Alternation Syntax
NM_001406789.1:c.1225G>A
ClinVar RefSeq Alternation Syntax
NM_001406764.1:c.2281G>A
ClinVar RefSeq Alternation Syntax
NM_001406785.1:c.1393G>A
ClinVar RefSeq Alternation Syntax
NM_001406781.1:c.1814C>G
ClinVar RefSeq Alternation Syntax
NM_001406765.1:c.2275G>A
ClinVar RefSeq Alternation Syntax
NM_001406791.1:c.1105G>A
ClinVar RefSeq Alternation Syntax
NM_001406761.1:c.2281G>A
ClinVar RefSeq Alternation Syntax
NM_020630.7:c.2410G>A
ClinVar RefSeq Alternation Syntax
NM_001406759.1:c.2410G>A
ClinVar RefSeq Alternation Syntax
NM_001406769.1:c.2315C>G
ClinVar RefSeq Alternation Syntax
NM_001406770.1:c.2423C>G
ClinVar RefSeq Alternation Syntax
NM_001406762.1:c.2281G>A
ClinVar RefSeq Alternation Syntax
NM_001406782.1:c.1814C>G
ClinVar RefSeq Alternation Syntax
NM_000323.2:c.2711C>G
ClinVar RefSeq Alternation Syntax
NM_001406744.1:c.2410G>A
ClinVar RefSeq Alternation Syntax
NM_001406787.1:c.1679C>G
ClinVar RefSeq Alternation Syntax
NM_001406783.1:c.1685C>G
ClinVar RefSeq Alternation Syntax
NM_001406743.1:c.2410G>A
ClinVar RefSeq Alternation Syntax
NM_001406775.1:c.1985C>G
ClinVar RefSeq Alternation Syntax
NM_001406793.1:c.961G>A
ClinVar RefSeq Alternation Syntax
NM_001406760.1:c.2410G>A
ClinVar RefSeq Alternation Syntax
NM_001406777.1:c.1985C>G
ClinVar RefSeq Alternation Syntax
NM_001406774.1:c.1885G>A
ClinVar RefSeq Alternation Syntax
NM_001406776.1:c.1985C>G
ClinVar RefSeq Alternation Syntax
NM_001406786.1:c.1685C>G
ClinVar RefSeq Alternation Syntax
NM_001406771.1:c.1972G>A
ClinVar RefSeq Alternation Syntax
NM_001406785.1:c.1694C>G
ClinVar RefSeq Alternation Syntax
NM_001406766.1:c.2423C>G
ClinVar RefSeq Alternation Syntax
NM_001406794.1:c.1262C>G
ClinVar RefSeq Alternation Syntax
NM_001406790.1:c.1225G>A
ClinVar RefSeq Alternation Syntax
NM_020630.7:c.2711C>G
ClinVar RefSeq Alternation Syntax
NM_000323.2:c.2410G>A
ClinVar RefSeq Alternation Syntax
NM_001406779.1:c.1814C>G
ClinVar RefSeq Alternation Syntax
NM_001406767.1:c.2423C>G
ClinVar RefSeq Alternation Syntax
NM_001406783.1:c.1384G>A
ClinVar RefSeq Alternation Syntax
NM_001406787.1:c.1378G>A
ClinVar RefSeq Alternation Syntax
NM_001406743.1:c.2711C>G
ClinVar RefSeq Alternation Syntax
NM_001406784.1:c.1420G>A
ClinVar RefSeq Alternation Syntax
NM_001406794.1:c.961G>A
ClinVar RefSeq Alternation Syntax
NM_001406744.1:c.2711C>G
ClinVar RefSeq Alternation Syntax
NM_001355216.2:c.1949C>G
ClinVar RefSeq Alternation Syntax
NM_001406775.1:c.1684G>A
ClinVar RefSeq Alternation Syntax
NM_001406776.1:c.1684G>A
ClinVar RefSeq Alternation Syntax
NM_001406760.1:c.2711C>G
ClinVar RefSeq Alternation Syntax
NM_001406763.1:c.2576C>G
ClinVar RefSeq Alternation Syntax
NM_001406786.1:c.1384G>A
ClinVar RefSeq Alternation Syntax
NM_001406766.1:c.2122G>A
ClinVar RefSeq Alternation Syntax
NM_001406767.1:c.2122G>A
ClinVar RefSeq Alternation Syntax
NM_001406778.1:c.1985C>G
ClinVar RefSeq Alternation Syntax
NM_020629.2:c.2711C>G
ClinVar RefSeq Alternation Syntax
NM_001406790.1:c.1526C>G
ClinVar RefSeq Alternation Syntax
NM_001406779.1:c.1513G>A
ClinVar RefSeq Alternation Syntax
NM_001406768.1:c.2447C>G
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2002-01-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000014972
ClinVar Disease
Multiple endocrine neoplasia type 2B
Observed Origin Sample
germline
Pubmed
11788682
Drugs