Annotation Detail

Information
Associated Genes
KIT
Associated Variants
KIT p.Pro552_Val556del (p.P552_V556del) ( ENST00000687109.1, ENST00000687246.1, ENST00000288135.6, ENST00000412167.7, ENST00000686011.1, ENST00000687295.1, ENST00000689832.1, ENST00000689994.1, ENST00000690543.1, ENST00000692783.1 )
KIT p.Pro552_Val556del (p.P552_V556del) ( ENST00000288135.6, ENST00000412167.7, ENST00000686011.1, ENST00000687109.1, ENST00000687246.1, ENST00000687295.1, ENST00000689832.1, ENST00000689994.1, ENST00000690543.1, ENST00000692783.1 )
Associated Disease
gastrointestinal stromal tumor
Source Database
ClinVar
Description
NM_000222.3(KIT):c.1652_1666del (p.Pro551_Val555del) AND Gastrointestinal stromal tumor
ClinVar Allele ID
28893
ClinVar RefSeq Alternation Syntax
NM_001385286.1:c.1640_1654del
ClinVar RefSeq Alternation Syntax
NM_000222.3:c.1652_1666del
ClinVar RefSeq Alternation Syntax
NM_001385285.1:c.1652_1666del
ClinVar RefSeq Alternation Syntax
NM_001093772.2:c.1640_1654del
ClinVar RefSeq Alternation Syntax
NM_001385292.1:c.1643_1657del
ClinVar RefSeq Alternation Syntax
NM_001385288.1:c.1643_1657del
ClinVar RefSeq Alternation Syntax
NM_001385284.1:c.1655_1669del
ClinVar RefSeq Alternation Syntax
NM_001385290.1:c.1655_1669del
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
1998-01-23
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000014868
ClinVar Disease
Gastrointestinal stromal tumor
Observed Origin Sample
somatic
Pubmed
9438854
Drugs