Annotation Detail

Information
Associated Genes
RB1
Associated Variants
RB1 p.Glu587ValfsTer21 (p.E587Vfs*21) ( ENST00000713858.1, ENST00000713857.1, ENST00000650461.1, ENST00000267163.6, ENST00000713856.1 )
RB1 p.Glu587ValfsTer21 (p.E587Vfs*21) ( ENST00000267163.6, ENST00000650461.1, ENST00000713856.1, ENST00000713857.1, ENST00000713858.1 )
Associated Disease
retinoblastoma
Source Database
ClinVar
Description
NM_000321.3(RB1):c.1760_1769del (p.Glu587fs) AND Retinoblastoma
ClinVar Allele ID
28121
ClinVar RefSeq Alternation Syntax
NM_000321.3:c.1760_1769del
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
1989-11-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000013957
ClinVar Disease
Retinoblastoma
Observed Origin Sample
germline
Pubmed
2601691
Drugs