Annotation Detail

Information
Associated Genes
PAH
Associated Variants
PAH p.Phe39Leu (p.F39L) ( ENST00000553106.6, ENST00000307000.7 )
PAH p.Phe39Leu (p.F39L) ( ENST00000307000.7, ENST00000553106.6 )
Associated Disease
phenylketonuria
Source Database
ClinVar
Description
NM_000277.3(PAH):c.117C>G (p.Phe39Leu) AND Phenylketonuria
ClinVar Allele ID
15644
ClinVar RefSeq Alternation Syntax
NM_000277.3:c.117C>G
ClinVar RefSeq Alternation Syntax
NM_001354304.2:c.117C>G
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2020-03-27
Clinical Significance Review Status
reviewed by expert panel
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000000636
ClinVar Disease
Phenylketonuria
Observed Origin Sample
germline
Observed Origin Sample
unknown
Pubmed
2063869
Drugs