Annotation Detail

Information
Associated Genes
ABL1
Associated Variants
ABL1 p.Thr334Ile (p.T334I) ABL1 p.Thr334Ile (p.T334I)
Associated Disease
acute lymphoblastic leukemia
Source Database
CIViC Evidence
Description
Bone marrow mononuclear cells (BM MNCs) were isolated from three acute lymphoblastic leukemia patients with the BCR-ABL1 T315I variant who were pretreated with various chemotherapeutics and dasatinib. 2/3 patient's BM MNCs were considered sensitive to ponatinib and axitinib using drug sensitivity scoring of proliferation assays. Additionally, BCR-ABL T315I showed sensitivity to ponitinib and axitinib in Ba/F3 cells.
Variant Origin
somatic
Variant Origin
Somatic
Evidence URL
https://civic.genome.wustl.edu/links/evidence_items/7777
Gene URL
https://civic.genome.wustl.edu/links/genes/4
Variant URL
https://civic.genome.wustl.edu/links/variants/2
Rating
3
Evidence Type
Predictive
Disease
Acute Lymphoblastic Leukemia
Evidence Direction
Does Not Support
Drug
Ponatinib,Axitinib
Evidence Level
D
Clinical Significance
Resistance
Pubmed
25686603
Drugs
Drug NameSensitivitySupported
AxitinibResitance or Non-Reponsefalse
PonatinibResitance or Non-Reponsefalse