Annotation Detail

Information
Associated Genes
VHL
Associated Variants
VHL p.Ser65Leu (p.S65L) ( ENST00000256474.3, ENST00000345392.3, ENST00000696143.2, ENST00000696153.1, ENST00000713811.1, ENST00000713812.1, ENST00000713815.1, ENST00000713982.1 )
VHL p.Ser65Leu (p.S65L) ( ENST00000256474.3, ENST00000345392.3, ENST00000696143.2, ENST00000696153.1, ENST00000713811.1, ENST00000713812.1, ENST00000713815.1, ENST00000713982.1 )
Associated Disease
clear cell renal cell carcinoma
Source Database
CIViC Evidence
Description
This study analyzed tumor and non-tumor kidney tissue from 195 unrelated patients with sporadic clear cell renal cell carcinoma (CCRCC) for a relationship between VHL variants in sporadic CCRCC and 'genotypes for genes encoding several carcinogen-metabolizing enzymes.' Higher frequency of VHL transversion variants was found in patients with presence of GETT1 and defective NAT1. This missense variant was found in a 68 year-old male (tumour 311).
Variant Origin
somatic
Variant Origin
Somatic
Evidence URL
https://civic.genome.wustl.edu/links/evidence_items/6131
Gene URL
https://civic.genome.wustl.edu/links/genes/58
Variant URL
https://civic.genome.wustl.edu/links/variants/1788
Rating
2
Evidence Type
Predisposing
Disease
Clear Cell Renal Cell Carcinoma
Evidence Direction
Supports
Evidence Level
E
Clinical Significance
Uncertain Significance
Pubmed
11505222
Drugs