chr3:33093471:C>A Detail (hg19) (GLB1)
Information
Genome
Assembly | Position |
---|---|
hg19 | chr3:33,093,471-33,093,471 |
hg38 | chr3:33,051,979-33,051,979 View the variant detail on this assembly version. |
HGVS
Type | Transcript | Protein |
---|---|---|
RefSeq | NM_000404.3:c.818G>T | NP_000395.2:p.Trp273Leu |
NM_001317040.1:c.818G>T | NP_001303969.1:p.Trp273Leu | |
NM_001135602.2:c.425G>T | NP_001129074.1:p.Trp142Leu |
Summary
MGeND
Clinical significance | |
Variant entry | |
GWAS entry | |
Disease area statistics | Show details |
Frequency
JP | HGVD:[No Data.] |
ToMMo:[No Data.] | |
NCBN:[No Data.] | |
NCBN(Hondo):[No Data.] | |
NCBN(Ryukyu):[No Data.] | |
East asia | ExAC:<0.001 |
Prediction
ClinVar
Clinical Significance |
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Review star | ![]() |
Show details |
Disease area statistics
[No Data.]
MGeND
[No Data.]
ClinVar
Clinical significance | Last evaluated | Review status | Condition | Origin | Links |
---|---|---|---|---|---|
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2001-08-01 | no assertion criteria provided | Mucopolysaccharidosis, MPS-IV-B |
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Detail |
CIViC
[No Data.]
DisGeNET
Score | Disease name | Description | Source | Pubmed | Links |
---|---|---|---|---|---|
0.367 | mucopolysaccharidosis type IVB | Apparently normal elastogenesis and EBP mRNA expression were observed for fibrob... | BeFree | 16538002 | Detail |
0.126 | Type I Mucolipidosis | Apparently normal elastogenesis and EBP mRNA expression were observed for fibrob... | BeFree | 16538002 | Detail |
0.003 | Type I Mucolipidosis | Apparently normal elastogenesis and EBP mRNA expression were observed for fibrob... | BeFree | 16538002 | Detail |
0.001 | galactosialidosis | Apparently normal elastogenesis and EBP mRNA expression were observed for fibrob... | BeFree | 16538002 | Detail |
0.567 | galactosialidosis | Apparently normal elastogenesis and EBP mRNA expression were observed for fibrob... | BeFree | 16538002 | Detail |
0.001 | Type I Mucolipidosis | Apparently normal elastogenesis and EBP mRNA expression were observed for fibrob... | BeFree | 16538002 | Detail |
0.004 | galactosialidosis | Apparently normal elastogenesis and EBP mRNA expression were observed for fibrob... | BeFree | 16538002 | Detail |
0.367 | mucopolysaccharidosis type IVB | NA | CLINVAR | Detail | |
0.367 | mucopolysaccharidosis type IVB | Mutation analyses in 17 patients with deficiency in acid beta-galactosidase: thr... | BeFree | 11511921 | Detail |
Annotation
Annotations
Descrption | Source | Links |
---|---|---|
NM_000404.4(GLB1):c.818G>T (p.Trp273Leu) AND Mucopolysaccharidosis, MPS-IV-B | ClinVar | Detail |
Apparently normal elastogenesis and EBP mRNA expression were observed for fibroblasts from Morquio B... | DisGeNET | Detail |
Apparently normal elastogenesis and EBP mRNA expression were observed for fibroblasts from Morquio B... | DisGeNET | Detail |
Apparently normal elastogenesis and EBP mRNA expression were observed for fibroblasts from Morquio B... | DisGeNET | Detail |
Apparently normal elastogenesis and EBP mRNA expression were observed for fibroblasts from Morquio B... | DisGeNET | Detail |
Apparently normal elastogenesis and EBP mRNA expression were observed for fibroblasts from Morquio B... | DisGeNET | Detail |
Apparently normal elastogenesis and EBP mRNA expression were observed for fibroblasts from Morquio B... | DisGeNET | Detail |
Apparently normal elastogenesis and EBP mRNA expression were observed for fibroblasts from Morquio B... | DisGeNET | Detail |
NA | DisGeNET | Detail |
Mutation analyses in 17 patients with deficiency in acid beta-galactosidase: three novel point mutat... | DisGeNET | Detail |
Overlapped Transcript Coordinates
Gene | Transcript ID | Exon Number | Chromosome | Start | Stop | Type | Amino Mutation | Transcript Position | Links |
---|
Overlapped Transcript
Gene | Transcript ID | Chromosome | Start | Stop | Links |
---|
- Gene
- -
- dbSNP
- rs72555362 dbSNP
- Genome
- hg19
- Position
- chr3:33,093,471-33,093,471
- Variant Type
- snv
- Reference Allele
- C
- Alternative Allele
- A
- East Asian Chromosome Counts (ExAC)
- 8616
- East Asian Allele Counts (ExAC)
- 0
- East Asian Heterozygous Counts (ExAC)
- 0
- East Asian Homozygous Counts (ExAC)
- 0
- East Asian Allele Frequency (ExAC)
- 0.0
- Chromosome Counts in All Race (ExAC)
- 120710
- Allele Counts in All Race (ExAC)
- 6
- Heterozygous Counts in All Race (ExAC)
- 6
- Homozygous Counts in All Race (ExAC)
- 0
- Allele Frequency in All Race (ExAC)
- 4.9705906718581727E-5
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