nonspecific interstitial pneumonia

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Information
Disease name
nonspecific interstitial pneumonia
Disease ID
DOID:2801
Description
"An idiopathic interstitial pneumonia that occurs mainly in women, people who do not smoke, and people younger than 50 years with no known cause or risk factors. Lung biopsies may show predominantly interstitial inflammation or fibrosis or a combination of inflammation and fibrosis. A dry cough and shortness of breath develop over 6 to 18 months. Low-grade fever and a feeling of illness (malaise) may occur." [url:http\://www.merck.com/mmhe/sec04/ch050/ch050b.html?qt=idiopathic%20interstitial%20pneumonia&alt=sh]
Disease area statistics
[No Data.]
Chromosome band
[No Data.]
Annotation
Genes Mutation Description Source Links
NCT ID Status Phase Summary Start date Completion date
NCT02596841 Completed Lung Diffusing Capacity for Nitric Oxide as a Marker of Fibrotic Changes in Idiopathic Interstitial Pneumonias February 2013 August 2015
NCT03800017 Not yet recruiting N/A Skeletal Muscle Function in Interstitial Lung Disease June 1, 2024 December 31, 2026
NCT03836417 Recruiting Molecular Diagnosis of Idiopathic Interstitial Pneumonias: a Prospective Study June 28, 2019 June 30, 2025
NCT05007340 Recruiting ILD-SARDs Registry and Biorepository August 24, 2021 August 2026
NCT00637065 Unknown status Phase 4 Bosentan in Pulmonary Hypertension in Interstitial Lung Disease Treatment Study April 2008 August 2010
Disase is a (Disease Ontology)
DOID:2797
Cross Reference ID (Disease Ontology)
NCI:C35717
Cross Reference ID (Disease Ontology)
SNOMEDCT_US_2023_03_01:129452008
Cross Reference ID (Disease Ontology)
UMLS_CUI:C1290344
Exact Synonym (Disease Ontology)
NSIP
MedGen concept unique identifier (MedGen Concept name)
C1290344
MedGen unique identifier (MedGen Concept name)
220936