acute interstitial pneumonia

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Information
Disease name
acute interstitial pneumonia
Disease ID
DOID:2800
Description
"A idiopathic interstitial pneumonia which develops suddenly and is severe. Initially, the lung shows edema, hyaline membranes, and interstitial acute inflammation. Later, it develops loose organizing fibrosis, mostly within alveolar septa and type II pneumocyte hyperplasia. Fever, cough, and difficulty breathing develop over 1 to 2 weeks, typically progressing to acute respiratory failure." [url:http\://www.merck.com/mmhe/sec04/ch050/ch050b.html?qt=idiopathic%20interstitial%20pneumonia&alt=sh, url:https\://www.ncbi.nlm.nih.gov/pubmed/11790668]
Disease area statistics
[No Data.]
Chromosome band
[No Data.]
Annotation
Genes Mutation Description Source Links
Disase is a (Disease Ontology)
DOID:2797
Cross Reference ID (Disease Ontology)
GARD:12835
Cross Reference ID (Disease Ontology)
ICD10CM:J84.114
Cross Reference ID (Disease Ontology)
ICD9CM:516.33
Cross Reference ID (Disease Ontology)
NCI:C35806
Cross Reference ID (Disease Ontology)
ORDO:79126
Cross Reference ID (Disease Ontology)
SNOMEDCT_US_2023_03_01:129459004
Cross Reference ID (Disease Ontology)
UMLS_CUI:C1279945
Exact Synonym (Disease Ontology)
accelerated interstitial pneumonia
Exact Synonym (Disease Ontology)
acute interstitial pneumonitis
Exact Synonym (Disease Ontology)
AIP
Exact Synonym (Disease Ontology)
Hamman-Rich disease
Exact Synonym (Disease Ontology)
Hamman-Rich syndrome
Exact Synonym (Disease Ontology)
Idiopathic pulmonary fibrosis, acute fatal form
OrphaNumber from OrphaNet (Orphanet)
79126