desquamative interstitial pneumonia
Information
- Disease name
- desquamative interstitial pneumonia
- Disease ID
- DOID:0050158
- Description
- "An idiopathic interstitial pneumonia that is characterized by the accumulation of bronchiolocentric alveolar macrophages in alveolar spaces and interstitial inflammation and involves mild bronchiolar fibrosis and chronic inflammation." [url:http\://ncit.nci.nih.gov/ncitbrowser/ConceptReport.jsp?dictionary=NCI_Thesaurus&version=14.10d&code=C35288, url:http\://www.merck.com/mmhe/sec04/ch050/ch050b.html?qt=idiopathic%20interstitial%20pneumonia&alt=sh, url:https\://www.ncbi.nlm.nih.gov/pubmed/11790668, url:https\://www.ncbi.nlm.nih.gov/pubmed/16142185, url:https\://www.ncbi.nlm.nih.gov/pubmed/16456642, url:https\://www.ncbi.nlm.nih.gov/pubmed/23001799]
Disease area statistics
[No Data.]
Chromosome band
[No Data.]
Annotation
Genes | Mutation | Description | Source | Links |
---|
NCT ID | Status | Phase | Summary | Start date | Completion date |
---|---|---|---|---|---|
NCT02019641 | Completed | N/A | The NIH Exercise Therapy for Advanced Lung Disease Trials: Response and Adaptation to Aerobic Exercise in Patients With Interstitial Lung Disease | May 23, 2015 | May 24, 2023 |
NCT02036970 | Completed | Phase 2 | Bardoxolone Methyl Evaluation in Patients With Pulmonary Hypertension (PH) - LARIAT | May 31, 2014 | May 16, 2018 |
- Disase is a (Disease Ontology)
- DOID:2797
- Cross Reference ID (Disease Ontology)
- ICD10CM:J84.117
- Cross Reference ID (Disease Ontology)
- ICD9CM:516.37
- Cross Reference ID (Disease Ontology)
- MESH:C562470
- Cross Reference ID (Disease Ontology)
- MIM:263000
- Cross Reference ID (Disease Ontology)
- NCI:C35288
- Cross Reference ID (Disease Ontology)
- SNOMEDCT_US_2023_03_01:8549006
- Cross Reference ID (Disease Ontology)
- UMLS_CUI:C0238378
- Exact Synonym (Disease Ontology)
- familial desquamative interstitial pneumonitis
- Exact Synonym (Disease Ontology)
- RBILD
- Exact Synonym (Disease Ontology)
- respiratory bronchiolitis-associated interstitial lung disease