Annotation Detail

Information
Associated Genes
BBS1
Associated Variants
BBS1 p.Met390Arg (p.M390R), ENSG00000256349 p.Met427Arg (p.M427R) ( ENST00000393994.4, ENST00000630659.2, ENST00000318312.12, ENST00000455748.6, ENST00000526986.5 )
BBS1 p.Met390Arg (p.M390R), ENSG00000256349 p.Met427Arg (p.M427R) ( ENST00000318312.12, ENST00000393994.4, ENST00000455748.6, ENST00000630659.2, ENST00000526986.5 )
Associated Disease
Bardet-Biedl syndrome 1 (disorder)
Source Database
DisGeNET
Description
BBS genotype-phenotype assessment of a multiethnic patient cohort calls for a revision of the disease definition.
Pubmed
21344540
Original source reporting the Gene Disease association
UNIPROT
DisGENET score for the Gene Disease association
0.321085767488321
Year of publication
2011
Drugs