Annotation Detail

Information
Associated Genes
PKP2
Associated Variants
PKP2 p.Thr50SerfsTer61 (p.T50Sfs*61) ( ENST00000340811.9, ENST00000546741.3, ENST00000700563.2, ENST00000700564.2, ENST00000070846.11, ENST00000700559.2 )
PKP2 p.Thr50SerfsTer61 (p.T50Sfs*61) ( ENST00000340811.9, ENST00000546741.3, ENST00000700559.2, ENST00000700563.2, ENST00000700564.2, ENST00000070846.11 )
PKP2 c.2489+1G>T ( ENST00000340811.9, ENST00000700558.2, ENST00000700559.2, ENST00000549461.3, ENST00000070846.11 )
PKP2 c.2489+1G>C ( ENST00000340811.9, ENST00000070846.11, ENST00000549461.3, ENST00000700559.2, ENST00000700558.2 )
PKP2 c.2489+1G>A ( ENST00000700559.2, ENST00000700558.2, ENST00000070846.11, ENST00000549461.3, ENST00000340811.9 )
PKP2 c.2146-1G>C ( ENST00000549461.3, ENST00000070846.11, ENST00000700559.2, ENST00000700558.2, ENST00000340811.9 )
PKP2 p.Trp676Ter (p.W676*) ( ENST00000070846.11, ENST00000700564.2, ENST00000549461.3, ENST00000700562.2, ENST00000700559.2, ENST00000700558.2, ENST00000340811.9, ENST00000700563.2 )
PKP2 p.Trp538Ter (p.W538*) ( ENST00000700559.2, ENST00000700564.2, ENST00000070846.11, ENST00000700563.2, ENST00000340811.9 )
PKP2 c.1378+1G>C ( ENST00000700559.2, ENST00000700564.2, ENST00000070846.11, ENST00000700563.2, ENST00000340811.9 )
PKP2 p.Arg413Ter (p.R413*) ( ENST00000700563.2, ENST00000340811.9, ENST00000700559.2, ENST00000700564.2, ENST00000070846.11 )
PKP2 p.Leu360Pro (p.L360P) ( ENST00000700563.2, ENST00000340811.9, ENST00000700559.2, ENST00000700564.2, ENST00000070846.11 )
PKP2 c.2489+1G>T ( ENST00000070846.11, ENST00000340811.9, ENST00000549461.3, ENST00000700558.2, ENST00000700559.2 )
PKP2 c.2489+1G>C ( ENST00000070846.11, ENST00000340811.9, ENST00000549461.3, ENST00000700558.2, ENST00000700559.2 )
PKP2 c.2489+1G>A ( ENST00000070846.11, ENST00000340811.9, ENST00000549461.3, ENST00000700558.2, ENST00000700559.2 )
PKP2 c.2146-1G>C ( ENST00000070846.11, ENST00000340811.9, ENST00000549461.3, ENST00000700558.2, ENST00000700559.2 )
PKP2 p.Trp676Ter (p.W676*) ( ENST00000070846.11, ENST00000340811.9, ENST00000549461.3, ENST00000700558.2, ENST00000700559.2, ENST00000700562.2, ENST00000700563.2, ENST00000700564.2 )
PKP2 p.Trp538Ter (p.W538*) ( ENST00000070846.11, ENST00000340811.9, ENST00000700559.2, ENST00000700563.2, ENST00000700564.2 )
PKP2 c.1378+1G>C ( ENST00000070846.11, ENST00000340811.9, ENST00000700559.2, ENST00000700563.2, ENST00000700564.2 )
PKP2 p.Arg413Ter (p.R413*) ( ENST00000070846.11, ENST00000340811.9, ENST00000700559.2, ENST00000700563.2, ENST00000700564.2 )
PKP2 p.Leu360Pro (p.L360P) ( ENST00000070846.11, ENST00000340811.9, ENST00000700559.2, ENST00000700563.2, ENST00000700564.2 )
PKP2 p.Ser329LysfsTer7 (p.S329Kfs*7)
PKP2 p.Ser329LysfsTer7 (p.S329Kfs*7)
Associated Disease
Arrhythmogenic Right Ventricular Dysplasia
Source Database
DisGeNET
Description
NA
Original source reporting the Gene Disease association
CLINVAR
DisGENET score for the Gene Disease association
0.163220184922405
Year of publication
NA
Drugs