Annotation Detail

Information
Associated Genes
TARDBP
Associated Variants
TARDBP p.Gly287Ser (p.G287S) ( ENST00000700088.1, ENST00000621790.4, ENST00000240185.8, ENST00000649624.1, ENST00000629725.2, ENST00000315091.7, ENST00000616545.4, ENST00000639083.1 )
TARDBP p.Gly287Arg (p.G287R) ( ENST00000700088.1, ENST00000621790.4, ENST00000240185.8, ENST00000649624.1, ENST00000629725.2, ENST00000616545.4, ENST00000639083.1, ENST00000315091.7 )
TARDBP p.Gly295Ser (p.G295S) ( ENST00000621790.4, ENST00000700088.1, ENST00000240185.8, ENST00000629725.2, ENST00000649624.1, ENST00000639083.1, ENST00000616545.4, ENST00000315091.7 )
TARDBP p.Gly295Arg (p.G295R) ( ENST00000240185.8, ENST00000621790.4, ENST00000700088.1, ENST00000315091.7, ENST00000639083.1, ENST00000616545.4, ENST00000649624.1, ENST00000629725.2 )
TARDBP p.Ser332Asn (p.S332N) ( ENST00000621790.4, ENST00000700088.1, ENST00000240185.8, ENST00000649624.1, ENST00000629725.2, ENST00000315091.7, ENST00000639083.1, ENST00000616545.4 )
TARDBP p.Gly335Asp (p.G335D) ( ENST00000639083.1, ENST00000616545.4, ENST00000315091.7, ENST00000649624.1, ENST00000629725.2, ENST00000240185.8, ENST00000700088.1, ENST00000621790.4 )
TARDBP p.Met337Val (p.M337V) ( ENST00000621790.4, ENST00000700088.1, ENST00000240185.8, ENST00000629725.2, ENST00000649624.1, ENST00000616545.4, ENST00000639083.1, ENST00000315091.7 )
TARDBP p.Ser379Cys (p.S379C) ( ENST00000315091.7, ENST00000639083.1, ENST00000616545.4, ENST00000629725.2, ENST00000649624.1, ENST00000240185.8, ENST00000621790.4, ENST00000700088.1 )
TARDBP p.Ser393Leu (p.S393L) ( ENST00000700088.1, ENST00000315091.7, ENST00000621790.4, ENST00000240185.8, ENST00000629725.2, ENST00000649624.1, ENST00000616545.4, ENST00000639083.1 )
TARDBP p.Gly287Ser (p.G287S) ( ENST00000700088.1, ENST00000240185.8, ENST00000315091.7, ENST00000616545.4, ENST00000621790.4, ENST00000629725.2, ENST00000639083.1, ENST00000649624.1 )
TARDBP p.Gly287Arg (p.G287R) ( ENST00000700088.1, ENST00000240185.8, ENST00000315091.7, ENST00000616545.4, ENST00000621790.4, ENST00000629725.2, ENST00000639083.1, ENST00000649624.1 )
TARDBP p.Gly295Ser (p.G295S) ( ENST00000700088.1, ENST00000240185.8, ENST00000315091.7, ENST00000616545.4, ENST00000621790.4, ENST00000629725.2, ENST00000639083.1, ENST00000649624.1 )
TARDBP p.Gly295Arg (p.G295R) ( ENST00000700088.1, ENST00000240185.8, ENST00000315091.7, ENST00000616545.4, ENST00000621790.4, ENST00000629725.2, ENST00000639083.1, ENST00000649624.1 )
TARDBP p.Ser332Asn (p.S332N) ( ENST00000700088.1, ENST00000240185.8, ENST00000315091.7, ENST00000616545.4, ENST00000621790.4, ENST00000629725.2, ENST00000639083.1, ENST00000649624.1 )
TARDBP p.Gly335Asp (p.G335D) ( ENST00000700088.1, ENST00000240185.8, ENST00000315091.7, ENST00000616545.4, ENST00000621790.4, ENST00000629725.2, ENST00000639083.1, ENST00000649624.1 )
TARDBP p.Met337Val (p.M337V) ( ENST00000700088.1, ENST00000240185.8, ENST00000315091.7, ENST00000616545.4, ENST00000621790.4, ENST00000629725.2, ENST00000639083.1, ENST00000649624.1 )
TARDBP p.Ser379Cys (p.S379C) ( ENST00000700088.1, ENST00000240185.8, ENST00000315091.7, ENST00000616545.4, ENST00000621790.4, ENST00000629725.2, ENST00000639083.1, ENST00000649624.1 )
TARDBP p.Ser393Leu (p.S393L) ( ENST00000700088.1, ENST00000240185.8, ENST00000315091.7, ENST00000616545.4, ENST00000621790.4, ENST00000629725.2, ENST00000639083.1, ENST00000649624.1 )
Associated Disease
AMYOTROPHIC LATERAL SCLEROSIS 10 (disorder)
Source Database
DisGeNET
Description
High frequency of TARDBP gene mutations in Italian patients with amyotrophic lateral sclerosis.
Pubmed
19224587
Original source reporting the Gene Disease association
UNIPROT
DisGENET score for the Gene Disease association
0.24
Year of publication
2009
Drugs