Annotation Detail

Information
Associated Genes
INS
Associated Variants
KCNJ11 p.Arg201Leu (p.R201L) ( ENST00000528731.1, ENST00000339994.5, ENST00000682350.1, ENST00000682764.1 )
KCNJ11 p.Arg201His (p.R201H) ( ENST00000682764.1, ENST00000682350.1, ENST00000339994.5, ENST00000528731.1 )
KCNJ11 p.Arg201Leu (p.R201L) ( ENST00000339994.5, ENST00000528731.1, ENST00000682350.1, ENST00000682764.1 )
KCNJ11 p.Arg201His (p.R201H) ( ENST00000339994.5, ENST00000528731.1, ENST00000682350.1, ENST00000682764.1 )
Associated Disease
DIABETES MELLITUS, PERMANENT NEONATAL
Source Database
DisGeNET
Description
Unsuccessful switch from insulin to sulfonylurea therapy in permanent neonatal diabetes mellitus due to an R201H mutation in the KCNJ11 gene: a case report.
Pubmed
23434183
Original source reporting the Gene Disease association
BeFree
DisGENET score for the Gene Disease association
0.568414698034489
Year of publication
2013
Drugs