Annotation Detail

Information
Associated Genes
KCNJ11
Associated Variants
KCNJ11 p.Val59Gly (p.V59G) ( ENST00000528731.1, ENST00000682350.1, ENST00000682764.1, ENST00000339994.5 )
KCNJ11 p.Val59Gly (p.V59G) ( ENST00000339994.5, ENST00000528731.1, ENST00000682350.1, ENST00000682764.1 )
Associated Disease
DIABETES MELLITUS, PERMANENT NEONATAL
Source Database
DisGeNET
Description
We have verified a lack of clinical response for both glycemic control and neurological features in an infant with permanent neonatal diabetes mellitus and DEND syndrome due to a V59A mutation in the KCNJ11 gene.
Pubmed
23382304
Original source reporting the Gene Disease association
BeFree
DisGENET score for the Gene Disease association
0.56868613990657
Year of publication
2013
Drugs