Annotation Detail

Information
Associated Genes
KCNJ11
Associated Variants
KCNJ11 p.Gly53Asp (p.G53D) ( ENST00000528731.1, ENST00000682764.1, ENST00000682350.1, ENST00000339994.5 )
KCNJ11 p.Gly53Asp (p.G53D) ( ENST00000339994.5, ENST00000528731.1, ENST00000682350.1, ENST00000682764.1 )
Associated Disease
Neonatal diabetes mellitus
Source Database
DisGeNET
Description
The G53D mutation in Kir6.2 (KCNJ11) is associated with neonatal diabetes and motor dysfunction in adulthood that is improved with sulfonylurea therapy.
Pubmed
18073297
Original source reporting the Gene Disease association
BeFree
DisGENET score for the Gene Disease association
0.149315722184673
Year of publication
2008
Drugs