Annotation Detail

Information
Associated Genes
GJB2
Associated Variants
GJB2 p.Arg184Pro (p.R184P) ( ENST00000382844.2, ENST00000382848.5 )
GJB2 p.Arg184Gln (p.R184Q) ( ENST00000382844.2, ENST00000382848.5 )
GJB2 p.Arg184Pro (p.R184P) ( ENST00000382844.2, ENST00000382848.5 )
GJB2 p.Arg184Gln (p.R184Q) ( ENST00000382844.2, ENST00000382848.5 )
Associated Disease
Hearing Loss, Mixed Conductive-Sensorineural
Source Database
DisGeNET
Description
Mutation R184Q of connexin 26 in hearing loss patients has a dominant-negative effect on connexin 26 and connexin 30.
Pubmed
20442751
Original source reporting the Gene Disease association
BeFree
DisGENET score for the Gene Disease association
0.0646031655551122
Year of publication
2010
Drugs