Annotation Detail

Information
Associated Genes
ARSA
Associated Variants
ARSA p.Thr411Ile (p.T411I) ( ENST00000216124.10, ENST00000395619.3, ENST00000356098.9, ENST00000395621.7, ENST00000453344.6 )
ARSA p.Gly101Val (p.G101V) ( ENST00000216124.10, ENST00000356098.9, ENST00000395619.3, ENST00000395621.7, ENST00000453344.6 )
ARSA p.Gly101Asp (p.G101D) ( ENST00000216124.10, ENST00000395621.7, ENST00000356098.9, ENST00000453344.6, ENST00000395619.3 )
ARSA p.Thr411Ile (p.T411I) ( ENST00000356098.9, ENST00000453344.6, ENST00000395621.7, ENST00000395619.3, ENST00000216124.10 )
ARSA p.Gly101Val (p.G101V) ( ENST00000216124.10, ENST00000356098.9, ENST00000395619.3, ENST00000395621.7, ENST00000453344.6 )
ARSA p.Gly101Asp (p.G101D) ( ENST00000356098.9, ENST00000395619.3, ENST00000216124.10, ENST00000395621.7, ENST00000453344.6 )
Associated Disease
Leukodystrophy, Metachromatic
Source Database
DisGeNET
Description
She was diagnosed with MLD by genetic analysis, which revealed compound heterozygous ARSA missense mutations (p.G99D and p.T409I).
Pubmed
21265945
Original source reporting the Gene Disease association
UNIPROT
DisGENET score for the Gene Disease association
0.514051056554323
Year of publication
2011
Drugs