Annotation Detail

Information
Associated Genes
PRNP
Associated Variants
PRNP p.Met232Arg (p.M232R) ( ENST00000424424.2, ENST00000379440.9, ENST00000430350.2, ENST00000457586.2 )
PRNP p.Met232Arg (p.M232R) ( ENST00000430350.2, ENST00000379440.9, ENST00000424424.2, ENST00000457586.2 )
Associated Disease
Creutzfeldt-Jakob disease
Source Database
DisGeNET
Description
Patients with genetic Creutzfeldt-Jakob disease in which arginine is substituted for methionine at codon 232 (M232R) of the prion protein gene (CJD232) have been described in Japan, and a recent study has revealed the presence of two clinical phenotypes: a rapidly progressive type (rapid-type) and a slowly progressive type (slow-type).
Pubmed
19422537
Original source reporting the Gene Disease association
BeFree
DisGENET score for the Gene Disease association
0.858675488785102
Year of publication
2009
Drugs