Annotation Detail

Information
Associated Genes
PRNP
Associated Variants
PRNP p.Pro102Leu (p.P102L) ( ENST00000457586.2, ENST00000430350.2, ENST00000379440.9, ENST00000424424.2 )
PRNP p.Pro102Leu (p.P102L) ( ENST00000379440.9, ENST00000457586.2, ENST00000430350.2, ENST00000424424.2 )
Associated Disease
Gerstmann-Straussler-Scheinker Disease
Source Database
DisGeNET
Description
Hyperphosphorylated tau deposition parallels prion protein burden in a case of Gerstmann-Sträussler-Scheinker syndrome P102L mutation complicated with dementia.
Pubmed
12200619
Original source reporting the Gene Disease association
BeFree
DisGENET score for the Gene Disease association
0.600051301892636
Year of publication
2002
Drugs