Annotation Detail

Information
Associated Genes
PRNP
Associated Variants
PRNP p.Pro102Leu (p.P102L) ( ENST00000457586.2, ENST00000430350.2, ENST00000379440.9, ENST00000424424.2 )
PRNP p.Pro102Leu (p.P102L) ( ENST00000379440.9, ENST00000457586.2, ENST00000430350.2, ENST00000424424.2 )
Associated Disease
Gerstmann-Straussler-Scheinker Disease
Source Database
DisGeNET
Description
A mutation equivalent to P102L in the human PrP gene, associated with Gerstmann-Straussler syndrome (GSS), has been introduced into the murine PrP gene by gene targeting.
Pubmed
10581259
Original source reporting the Gene Disease association
BeFree
DisGENET score for the Gene Disease association
0.600051301892636
Year of publication
1999
Drugs