Annotation Detail

Information
Associated Genes
TREX1
Associated Variants
ATRIP c.*1442G>A, TREX1 p.Arg114His (p.R114H) ( ENST00000433541.1, ENST00000444177.1, ENST00000456089.1, ENST00000492235.2, ENST00000625293.3, ENST00000635452.2, ENST00000320211.10 )
ATRIP c.*1442G>C, TREX1 p.Arg114Pro (p.R114P) ( ENST00000433541.1, ENST00000444177.1, ENST00000456089.1, ENST00000492235.2, ENST00000625293.3, ENST00000635452.2, ENST00000320211.10 )
ATRIP c.*1442G>A, TREX1 p.Arg114His (p.R114H) ( ENST00000433541.1, ENST00000444177.1, ENST00000456089.1, ENST00000492235.2, ENST00000625293.3, ENST00000635452.2, ENST00000320211.10 )
ATRIP c.*1442G>C, TREX1 p.Arg114Pro (p.R114P) ( ENST00000433541.1, ENST00000444177.1, ENST00000456089.1, ENST00000492235.2, ENST00000625293.3, ENST00000635452.2, ENST00000320211.10 )
Associated Disease
Aicardi-Goutieres syndrome 1
Source Database
DisGeNET
Description
The TREX1 exonuclease R114H mutation in Aicardi-Goutières syndrome and lupus reveals dimeric structure requirements for DNA degradation activity.
Pubmed
21937424
Original source reporting the Gene Disease association
BeFree
DisGENET score for the Gene Disease association
0.445971721185767
Year of publication
2011
Drugs