Annotation Detail

Information
Associated Genes
GJB2
Associated Variants
GJB2 p.Leu79CysfsTer3 (p.L79Cfs*3) ( ENST00000382848.5, ENST00000382844.2 )
GJB2 p.Leu79CysfsTer3 (p.L79Cfs*3) ( ENST00000382844.2, ENST00000382848.5 )
GJB2 p.Val37Phe (p.V37F) ( ENST00000382844.2, ENST00000382848.5 )
GJB2 p.Val37Ile (p.V37I) ( ENST00000382848.5, ENST00000382844.2 )
GJB2 p.Val37Phe (p.V37F) ( ENST00000382844.2, ENST00000382848.5 )
GJB2 p.Val37Ile (p.V37I) ( ENST00000382844.2, ENST00000382848.5 )
Associated Disease
Hearing Loss, Mixed Conductive-Sensorineural
Source Database
DisGeNET
Description
A total of 199 (19.6%) babies were found to have at least 1 mutated allele on the NGS for deafness, 11 (1.1%) of whom were homozygous for GJB2 p.V37I, 6 (0.6%) compound heterozygous for GJB2 p.V37I and c.235delC, and 1 (0.1%) homoplasmic for m.1555A>G, who may potentially have hearing loss.
Pubmed
21811586
Original source reporting the Gene Disease association
BeFree
DisGENET score for the Gene Disease association
0.0646031655551122
Year of publication
2011
Drugs