Annotation Detail

Information
Associated Genes
PSEN1
Associated Variants
PSEN1 p.Met139Val (p.M139V) ( ENST00000700322.1, ENST00000700317.1, ENST00000324501.10, ENST00000700321.1, ENST00000700273.1, ENST00000700323.1, ENST00000700313.1, ENST00000557293.6, ENST00000700431.1, ENST00000394164.5, ENST00000700378.1, ENST00000700271.1, ENST00000700265.1, ENST00000700320.1, ENST00000700307.1, ENST00000700469.1, ENST00000700389.1, ENST00000700324.1, ENST00000357710.8, ENST00000700468.1, ENST00000554131.6, ENST00000700268.1, ENST00000700437.1, ENST00000557511.5, ENST00000700306.1, ENST00000394157.7, ENST00000553599.6, ENST00000700375.1, ENST00000556951.6, ENST00000700312.1, ENST00000700269.1, ENST00000700267.1 )
PSEN1 p.Ile143Phe (p.I143F) ( ENST00000700322.1, ENST00000700273.1, ENST00000700321.1, ENST00000700317.1, ENST00000324501.10, ENST00000700431.1, ENST00000700323.1, ENST00000557293.6, ENST00000700313.1, ENST00000700469.1, ENST00000700307.1, ENST00000700389.1, ENST00000700265.1, ENST00000700271.1, ENST00000394164.5, ENST00000700378.1, ENST00000700320.1, ENST00000700468.1, ENST00000554131.6, ENST00000700268.1, ENST00000700437.1, ENST00000557511.5, ENST00000700324.1, ENST00000357710.8, ENST00000394157.7, ENST00000700306.1, ENST00000700312.1, ENST00000553599.6, ENST00000556951.6, ENST00000700375.1, ENST00000700269.1, ENST00000700267.1 )
PSEN1 p.Gly209Val (p.G209V) ( ENST00000700322.1, ENST00000700321.1, ENST00000700273.1, ENST00000324501.10, ENST00000700317.1, ENST00000557293.6, ENST00000700313.1, ENST00000700323.1, ENST00000700389.1, ENST00000700469.1, ENST00000700307.1, ENST00000700320.1, ENST00000700271.1, ENST00000394164.5, ENST00000700378.1, ENST00000700265.1, ENST00000557511.5, ENST00000554131.6, ENST00000700268.1, ENST00000700437.1, ENST00000700468.1, ENST00000700324.1, ENST00000357710.8, ENST00000700306.1, ENST00000700312.1, ENST00000556951.6, ENST00000700375.1, ENST00000553599.6, ENST00000700267.1, ENST00000700269.1 )
PSEN1 p.Arg269His (p.R269H) ( ENST00000324501.10, ENST00000557511.5, ENST00000394164.5, ENST00000357710.8, ENST00000553599.6, ENST00000554131.6, ENST00000556951.6, ENST00000557293.6, ENST00000700265.1, ENST00000700267.1, ENST00000700268.1, ENST00000700269.1, ENST00000700271.1, ENST00000700273.1, ENST00000700306.1, ENST00000700307.1, ENST00000700312.1, ENST00000700313.1, ENST00000700317.1, ENST00000700320.1, ENST00000700321.1, ENST00000700322.1, ENST00000700323.1, ENST00000700324.1, ENST00000700375.1, ENST00000700378.1, ENST00000700389.1, ENST00000700437.1, ENST00000700468.1, ENST00000700469.1 )
PSEN1 p.Glu280Ala (p.E280A) ( ENST00000357710.8, ENST00000324501.10, ENST00000394164.5, ENST00000557511.5, ENST00000553599.6, ENST00000554131.6, ENST00000556951.6, ENST00000557293.6, ENST00000700265.1, ENST00000700267.1, ENST00000700268.1, ENST00000700269.1, ENST00000700271.1, ENST00000700273.1, ENST00000700306.1, ENST00000700307.1, ENST00000700312.1, ENST00000700313.1, ENST00000700317.1, ENST00000700320.1, ENST00000700321.1, ENST00000700322.1, ENST00000700323.1, ENST00000700324.1, ENST00000700375.1, ENST00000700378.1, ENST00000700389.1, ENST00000700437.1, ENST00000700468.1, ENST00000700469.1 )
PSEN1 p.Glu280Gly (p.E280G) ( ENST00000700306.1, ENST00000557511.5, ENST00000700268.1, ENST00000700437.1, ENST00000554131.6, ENST00000700468.1, ENST00000357710.8, ENST00000700324.1, ENST00000700267.1, ENST00000700269.1, ENST00000700312.1, ENST00000700375.1, ENST00000556951.6, ENST00000553599.6, ENST00000700321.1, ENST00000700273.1, ENST00000324501.10, ENST00000700317.1, ENST00000700322.1, ENST00000700389.1, ENST00000700307.1, ENST00000700469.1, ENST00000700320.1, ENST00000700378.1, ENST00000394164.5, ENST00000700271.1, ENST00000700265.1, ENST00000700313.1, ENST00000557293.6, ENST00000700323.1 )
PSEN1 p.Met139Val (p.M139V) ( ENST00000324501.10, ENST00000357710.8, ENST00000394157.7, ENST00000394164.5, ENST00000553599.6, ENST00000554131.6, ENST00000556951.6, ENST00000557293.6, ENST00000557511.5, ENST00000700265.1, ENST00000700267.1, ENST00000700268.1, ENST00000700269.1, ENST00000700271.1, ENST00000700273.1, ENST00000700306.1, ENST00000700307.1, ENST00000700312.1, ENST00000700313.1, ENST00000700317.1, ENST00000700320.1, ENST00000700321.1, ENST00000700322.1, ENST00000700323.1, ENST00000700324.1, ENST00000700375.1, ENST00000700378.1, ENST00000700389.1, ENST00000700431.1, ENST00000700437.1, ENST00000700468.1, ENST00000700469.1 )
PSEN1 p.Ile143Phe (p.I143F) ( ENST00000324501.10, ENST00000357710.8, ENST00000394157.7, ENST00000394164.5, ENST00000553599.6, ENST00000554131.6, ENST00000556951.6, ENST00000557293.6, ENST00000557511.5, ENST00000700265.1, ENST00000700267.1, ENST00000700268.1, ENST00000700269.1, ENST00000700271.1, ENST00000700273.1, ENST00000700306.1, ENST00000700307.1, ENST00000700312.1, ENST00000700313.1, ENST00000700317.1, ENST00000700320.1, ENST00000700321.1, ENST00000700322.1, ENST00000700323.1, ENST00000700324.1, ENST00000700375.1, ENST00000700378.1, ENST00000700389.1, ENST00000700431.1, ENST00000700437.1, ENST00000700468.1, ENST00000700469.1 )
PSEN1 p.Gly209Val (p.G209V) ( ENST00000324501.10, ENST00000357710.8, ENST00000394164.5, ENST00000553599.6, ENST00000554131.6, ENST00000556951.6, ENST00000557293.6, ENST00000557511.5, ENST00000700265.1, ENST00000700267.1, ENST00000700268.1, ENST00000700269.1, ENST00000700271.1, ENST00000700273.1, ENST00000700306.1, ENST00000700307.1, ENST00000700312.1, ENST00000700313.1, ENST00000700317.1, ENST00000700320.1, ENST00000700321.1, ENST00000700322.1, ENST00000700323.1, ENST00000700324.1, ENST00000700375.1, ENST00000700378.1, ENST00000700389.1, ENST00000700437.1, ENST00000700468.1, ENST00000700469.1 )
PSEN1 p.Arg269His (p.R269H) ( ENST00000324501.10, ENST00000357710.8, ENST00000394164.5, ENST00000553599.6, ENST00000554131.6, ENST00000556951.6, ENST00000557293.6, ENST00000557511.5, ENST00000700265.1, ENST00000700267.1, ENST00000700268.1, ENST00000700269.1, ENST00000700271.1, ENST00000700273.1, ENST00000700306.1, ENST00000700307.1, ENST00000700312.1, ENST00000700313.1, ENST00000700317.1, ENST00000700320.1, ENST00000700321.1, ENST00000700322.1, ENST00000700323.1, ENST00000700324.1, ENST00000700375.1, ENST00000700378.1, ENST00000700389.1, ENST00000700437.1, ENST00000700468.1, ENST00000700469.1 )
PSEN1 p.Glu280Ala (p.E280A) ( ENST00000324501.10, ENST00000357710.8, ENST00000394164.5, ENST00000553599.6, ENST00000554131.6, ENST00000556951.6, ENST00000557293.6, ENST00000557511.5, ENST00000700265.1, ENST00000700267.1, ENST00000700268.1, ENST00000700269.1, ENST00000700271.1, ENST00000700273.1, ENST00000700306.1, ENST00000700307.1, ENST00000700312.1, ENST00000700313.1, ENST00000700317.1, ENST00000700320.1, ENST00000700321.1, ENST00000700322.1, ENST00000700323.1, ENST00000700324.1, ENST00000700375.1, ENST00000700378.1, ENST00000700389.1, ENST00000700437.1, ENST00000700468.1, ENST00000700469.1 )
PSEN1 p.Glu280Gly (p.E280G) ( ENST00000324501.10, ENST00000357710.8, ENST00000394164.5, ENST00000553599.6, ENST00000554131.6, ENST00000556951.6, ENST00000557293.6, ENST00000557511.5, ENST00000700265.1, ENST00000700267.1, ENST00000700268.1, ENST00000700269.1, ENST00000700271.1, ENST00000700273.1, ENST00000700306.1, ENST00000700307.1, ENST00000700312.1, ENST00000700313.1, ENST00000700317.1, ENST00000700320.1, ENST00000700321.1, ENST00000700322.1, ENST00000700323.1, ENST00000700324.1, ENST00000700375.1, ENST00000700378.1, ENST00000700389.1, ENST00000700437.1, ENST00000700468.1, ENST00000700469.1 )
Associated Disease
Neurofibrillary degeneration (morphologic abnormality)
Source Database
DisGeNET
Description
Some of the PS1 mutations studied (M139V, I143F, G209V, R269H, E280A), but not others, were also associated with faster rates of NFT formation and accelerated neuronal loss in the majority of the patients who harboured them when compared with sporadic Alzheimer's disease patients.
Pubmed
10468510
Original source reporting the Gene Disease association
BeFree
DisGENET score for the Gene Disease association
0.00244297684872273
Year of publication
1999
Drugs