Annotation Detail

Information
Associated Genes
LMNA
Associated Variants
LMNA p.Arg225Ter (p.R225*) ( ENST00000361308.9, ENST00000504687.7, ENST00000677389.1, ENST00000368299.7, ENST00000448611.6, ENST00000676385.2, ENST00000368300.9, ENST00000682650.1, ENST00000675939.1, ENST00000675667.1, ENST00000368301.6, ENST00000473598.6, ENST00000683032.1, ENST00000368297.5 )
LMNA p.Arg225Ter (p.R225*) ( ENST00000361308.9, ENST00000368297.5, ENST00000368299.7, ENST00000368300.9, ENST00000368301.6, ENST00000448611.6, ENST00000473598.6, ENST00000504687.7, ENST00000675667.1, ENST00000675939.1, ENST00000676385.2, ENST00000677389.1, ENST00000682650.1, ENST00000683032.1 )
Associated Disease
Thromboembolism
Source Database
DisGeNET
Description
Our study confirmed that the p.R225X mutation leads to cardiac conduction disease with late or no development of DCM, underscoring the importance of this mutation in putative familial lone conduction disease. Nearly one third of LMNA mutation carriers had experienced a thromboembolic event.
Pubmed
18035086
Original source reporting the Gene Disease association
BeFree
DisGENET score for the Gene Disease association
0.000271441872080303
Year of publication
2007
Drugs