Annotation Detail

Information
Associated Genes
LMNA
Associated Variants
LMNA p.Met371Lys (p.M371K) ( ENST00000368300.9, ENST00000682650.1, ENST00000504687.7, ENST00000676385.2, ENST00000448611.6, ENST00000368299.7, ENST00000361308.9, ENST00000368297.5, ENST00000683032.1, ENST00000473598.6, ENST00000368301.6, ENST00000677389.1, ENST00000675939.1, ENST00000675667.1 )
LMNA p.Met371Lys (p.M371K) ( ENST00000361308.9, ENST00000368297.5, ENST00000368299.7, ENST00000368300.9, ENST00000368301.6, ENST00000448611.6, ENST00000473598.6, ENST00000504687.7, ENST00000675667.1, ENST00000675939.1, ENST00000676385.2, ENST00000677389.1, ENST00000682650.1, ENST00000683032.1 )
Associated Disease
Autosomal Dominant Emery-Dreifuss Muscular Dystrophy (disorder)
Source Database
DisGeNET
Description
We used the heart-selective alpha-myosin heavy chain promoter to drive expression in transgenic mice of human wild-type and M371K lamin A, which causes EDMD.
Pubmed
16825283
Original source reporting the Gene Disease association
BeFree
DisGENET score for the Gene Disease association
0.447057488674088
Year of publication
2006
Drugs