Annotation Detail

Information
Associated Genes
LMNA
Associated Variants
LMNA p.Arg527His (p.R527H) ( ENST00000675667.1, ENST00000675939.1, ENST00000677389.1, ENST00000368301.6, ENST00000683032.1, ENST00000473598.6, ENST00000368297.5, ENST00000368299.7, ENST00000361308.9, ENST00000448611.6, ENST00000676385.2, ENST00000504687.7, ENST00000368300.9, ENST00000682650.1 )
LMNA p.Arg527Pro (p.R527P) ( ENST00000504687.7, ENST00000368299.7, ENST00000448611.6, ENST00000368297.5, ENST00000368301.6, ENST00000368300.9, ENST00000361308.9, ENST00000473598.6, ENST00000675667.1, ENST00000675939.1, ENST00000676385.2, ENST00000677389.1, ENST00000682650.1, ENST00000683032.1 )
LMNA p.Arg527His (p.R527H) ( ENST00000361308.9, ENST00000368297.5, ENST00000368299.7, ENST00000368300.9, ENST00000368301.6, ENST00000448611.6, ENST00000473598.6, ENST00000504687.7, ENST00000675667.1, ENST00000675939.1, ENST00000676385.2, ENST00000677389.1, ENST00000682650.1, ENST00000683032.1 )
LMNA p.Arg527Pro (p.R527P) ( ENST00000361308.9, ENST00000368297.5, ENST00000368299.7, ENST00000368300.9, ENST00000368301.6, ENST00000448611.6, ENST00000473598.6, ENST00000504687.7, ENST00000675667.1, ENST00000675939.1, ENST00000676385.2, ENST00000677389.1, ENST00000682650.1, ENST00000683032.1 )
Associated Disease
Premature aging syndrome
Source Database
DisGeNET
Description
Mandibuloacral dysplasia type A (MADA; OMIM # 248370) is a premature ageing disease caused by the homozygous R527H mutation in the LMNA gene.
Pubmed
18604166
Original source reporting the Gene Disease association
BeFree
DisGENET score for the Gene Disease association
0.0200966300556066
Year of publication
2008
Drugs