Annotation Detail

Information
Associated Genes
LMNA
Associated Variants
LMNA p.Arg527His (p.R527H) ( ENST00000675667.1, ENST00000675939.1, ENST00000677389.1, ENST00000368301.6, ENST00000683032.1, ENST00000473598.6, ENST00000368297.5, ENST00000368299.7, ENST00000361308.9, ENST00000448611.6, ENST00000676385.2, ENST00000504687.7, ENST00000368300.9, ENST00000682650.1 )
LMNA p.Arg527Pro (p.R527P) ( ENST00000504687.7, ENST00000368299.7, ENST00000448611.6, ENST00000368297.5, ENST00000368301.6, ENST00000368300.9, ENST00000361308.9, ENST00000473598.6, ENST00000675667.1, ENST00000675939.1, ENST00000676385.2, ENST00000677389.1, ENST00000682650.1, ENST00000683032.1 )
LMNA p.Arg527His (p.R527H) ( ENST00000361308.9, ENST00000368297.5, ENST00000368299.7, ENST00000368300.9, ENST00000368301.6, ENST00000448611.6, ENST00000473598.6, ENST00000504687.7, ENST00000675667.1, ENST00000675939.1, ENST00000676385.2, ENST00000677389.1, ENST00000682650.1, ENST00000683032.1 )
LMNA p.Arg527Pro (p.R527P) ( ENST00000361308.9, ENST00000368297.5, ENST00000368299.7, ENST00000368300.9, ENST00000368301.6, ENST00000448611.6, ENST00000473598.6, ENST00000504687.7, ENST00000675667.1, ENST00000675939.1, ENST00000676385.2, ENST00000677389.1, ENST00000682650.1, ENST00000683032.1 )
Associated Disease
Mandibuloacral dysostosis
Source Database
DisGeNET
Description
Analysis of the effect of the prevalent MAD mutation (R527H) over the transcriptional pattern of genes expressed in the human dermis showed that this LMNA gene mutation has pleiotropic effects on a limited number of genes.
Pubmed
15473259
Original source reporting the Gene Disease association
BeFree
DisGENET score for the Gene Disease association
0.485428837441606
Year of publication
2004
Drugs