Annotation Detail

Information
Associated Genes
UGT1A1
Associated Variants
UGT1A6 c.862-6500T>A, UGT1A5 c.868-6500T>A, UGT1A9 c.856-6500T>A, UGT1A7 c.856-6500T>A, UGT1A4 c.868-6500T>A, UGT1A8 c.856-6500T>A, UGT1A10 c.856-6500T>A, UGT1A3 c.868-6500T>A, UGT1A1 p.Phe83Ile (p.F83I) ( ENST00000344644.10, ENST00000373445.1, ENST00000373450.5, ENST00000373426.4, ENST00000305139.11, ENST00000373424.5, ENST00000406651.1, ENST00000373414.4, ENST00000354728.5, ENST00000373409.8, ENST00000305208.10, ENST00000360418.4, ENST00000482026.6 )
UGT1A6 c.862-6500T>C, UGT1A5 c.868-6500T>C, UGT1A9 c.856-6500T>C, UGT1A7 c.856-6500T>C, UGT1A4 c.868-6500T>C, UGT1A8 c.856-6500T>C, UGT1A10 c.856-6500T>C, UGT1A3 c.868-6500T>C, UGT1A1 p.Phe83Leu (p.F83L) ( ENST00000344644.10, ENST00000373445.1, ENST00000373450.5, ENST00000373426.4, ENST00000305139.11, ENST00000373424.5, ENST00000406651.1, ENST00000373414.4, ENST00000354728.5, ENST00000373409.8, ENST00000305208.10, ENST00000360418.4, ENST00000482026.6 )
UGT1A6 c.862-6500T>A, UGT1A5 c.868-6500T>A, UGT1A9 c.856-6500T>A, UGT1A7 c.856-6500T>A, UGT1A4 c.868-6500T>A, UGT1A8 c.856-6500T>A, UGT1A10 c.856-6500T>A, UGT1A3 c.868-6500T>A, UGT1A1 p.Phe83Ile (p.F83I) ( ENST00000344644.10, ENST00000373445.1, ENST00000373450.5, ENST00000373426.4, ENST00000305139.11, ENST00000373424.5, ENST00000406651.1, ENST00000373414.4, ENST00000354728.5, ENST00000373409.8, ENST00000305208.10, ENST00000360418.4, ENST00000482026.6 )
UGT1A6 c.862-6500T>C, UGT1A5 c.868-6500T>C, UGT1A9 c.856-6500T>C, UGT1A7 c.856-6500T>C, UGT1A4 c.868-6500T>C, UGT1A8 c.856-6500T>C, UGT1A10 c.856-6500T>C, UGT1A3 c.868-6500T>C, UGT1A1 p.Phe83Leu (p.F83L) ( ENST00000344644.10, ENST00000373445.1, ENST00000373450.5, ENST00000373426.4, ENST00000305139.11, ENST00000373424.5, ENST00000406651.1, ENST00000373414.4, ENST00000354728.5, ENST00000373409.8, ENST00000305208.10, ENST00000360418.4, ENST00000482026.6 )
Associated Disease
Gilbert Disease (disorder)
Source Database
DisGeNET
Description
Novel missense mutation of the UGT1A1 gene in Thai siblings with Gilbert's syndrome.
Pubmed
12139570
Original source reporting the Gene Disease association
UNIPROT
DisGENET score for the Gene Disease association
0.29501695686041
Year of publication
2002
Drugs