Annotation Detail

Information
Associated Genes
TNNT2
Associated Variants
TNNT2 p.Arg215Trp (p.R215W) ( ENST00000367318.10, ENST00000412633.3, ENST00000509001.5, ENST00000714313.1, ENST00000714314.1, ENST00000714312.1, ENST00000714316.2, ENST00000438742.6, ENST00000656932.1, ENST00000455702.7, ENST00000714317.1, ENST00000660295.1, ENST00000422165.6, ENST00000658476.1, ENST00000367322.6, ENST00000367320.6 )
TNNT2 p.Arg215= (p.R215=) ( ENST00000367318.10, ENST00000438742.6, ENST00000714316.2, ENST00000714312.1, ENST00000714314.1, ENST00000714313.1, ENST00000367320.6, ENST00000658476.1, ENST00000367322.6, ENST00000509001.5, ENST00000422165.6, ENST00000660295.1, ENST00000455702.7, ENST00000714317.1, ENST00000656932.1, ENST00000412633.3 )
TNNT2 p.Arg215Trp (p.R215W) ( ENST00000367318.10, ENST00000367320.6, ENST00000367322.6, ENST00000412633.3, ENST00000422165.6, ENST00000438742.6, ENST00000455702.7, ENST00000509001.5, ENST00000656932.1, ENST00000658476.1, ENST00000660295.1, ENST00000714312.1, ENST00000714313.1, ENST00000714314.1, ENST00000714316.2, ENST00000714317.1 )
TNNT2 p.Arg215= (p.R215=) ( ENST00000367318.10, ENST00000367320.6, ENST00000367322.6, ENST00000412633.3, ENST00000422165.6, ENST00000438742.6, ENST00000455702.7, ENST00000509001.5, ENST00000656932.1, ENST00000658476.1, ENST00000660295.1, ENST00000714312.1, ENST00000714313.1, ENST00000714314.1, ENST00000714316.2, ENST00000714317.1 )
Associated Disease
Cardiomyopathy, Dilated
Source Database
DisGeNET
Description
A c.517T C>T, Arg173Trp TNNT2 variant segregated with all affected family members and was also detected in one additional DCM family in our registry.
Pubmed
24205113
Original source reporting the Gene Disease association
BeFree
DisGENET score for the Gene Disease association
0.255635346102134
Year of publication
2013
Drugs