Annotation Detail

Information
Associated Genes
SCN5A
Associated Variants
SCN5A p.Arg1193Gln (p.R1193Q) ( ENST00000413689.6, ENST00000333535.9, ENST00000414099.6, ENST00000423572.7, ENST00000449557.6, ENST00000450102.6, ENST00000455624.6 )
SCN5A p.Arg1193Gln (p.R1193Q) ( ENST00000333535.9, ENST00000413689.6, ENST00000414099.6, ENST00000423572.7, ENST00000449557.6, ENST00000450102.6, ENST00000455624.6 )
Associated Disease
Channelopathies
Source Database
DisGeNET
Description
We report a Korean case of an overlap syndrome of cardiac sodium channelopathy with SCN5A p.R1193Q polymorphism, treated by the placement of an intrapericardial implantable cardioverter-defibrillator (ICD) at the age of 27 months.
Pubmed
22519808
Original source reporting the Gene Disease association
BeFree
DisGENET score for the Gene Disease association
0.00833875316436871
Year of publication
2012
Drugs