Annotation Detail

Information
Associated Genes
PRKDC
Associated Variants
BRCA1 p.Asp693Tyr (p.D693Y) ( ENST00000644379.2, ENST00000713676.1, ENST00000491747.6, ENST00000470026.6, ENST00000618469.2, ENST00000586385.5, ENST00000634433.2, ENST00000591849.5, ENST00000489037.2, ENST00000476777.6, ENST00000700182.1, ENST00000478531.6, ENST00000484087.6, ENST00000494123.6, ENST00000493795.5, ENST00000468300.5, ENST00000644555.2, ENST00000473961.6, ENST00000477152.6, ENST00000352993.7, ENST00000493919.6, ENST00000497488.2, ENST00000471181.7, ENST00000591534.5, ENST00000461574.2, ENST00000357654.9 )
BRCA1 p.Asp693Asn (p.D693N) ( ENST00000468300.5, ENST00000470026.6, ENST00000471181.7, ENST00000491747.6, ENST00000357654.9, ENST00000484087.6, ENST00000493795.5, ENST00000476777.6, ENST00000473961.6, ENST00000494123.6, ENST00000477152.6, ENST00000478531.6, ENST00000586385.5, ENST00000591534.5, ENST00000461574.2, ENST00000352993.7, ENST00000493919.6, ENST00000489037.2, ENST00000497488.2, ENST00000591849.5, ENST00000618469.2, ENST00000634433.2, ENST00000644379.2, ENST00000644555.2, ENST00000700182.1, ENST00000713676.1 )
WRN p.Val114Ile (p.V114I) ( ENST00000298139.7 )
PRKDC c.4412+39T>C ( ENST00000314191.7, ENST00000338368.7 )
PRKDC c.3847-634A>G ( ENST00000314191.7, ENST00000338368.7 )
PRKDC c.1623+6A>G ( ENST00000314191.7, ENST00000338368.7 )
BRCA1 p.Asp693Tyr (p.D693Y) ( ENST00000352993.7, ENST00000357654.9, ENST00000461574.2, ENST00000468300.5, ENST00000470026.6, ENST00000471181.7, ENST00000473961.6, ENST00000476777.6, ENST00000477152.6, ENST00000478531.6, ENST00000484087.6, ENST00000489037.2, ENST00000491747.6, ENST00000493795.5, ENST00000493919.6, ENST00000494123.6, ENST00000497488.2, ENST00000586385.5, ENST00000591534.5, ENST00000591849.5, ENST00000618469.2, ENST00000634433.2, ENST00000644379.2, ENST00000644555.2, ENST00000700182.1, ENST00000713676.1 )
BRCA1 p.Asp693Asn (p.D693N) ( ENST00000352993.7, ENST00000357654.9, ENST00000461574.2, ENST00000468300.5, ENST00000470026.6, ENST00000471181.7, ENST00000473961.6, ENST00000476777.6, ENST00000477152.6, ENST00000478531.6, ENST00000484087.6, ENST00000489037.2, ENST00000491747.6, ENST00000493795.5, ENST00000493919.6, ENST00000494123.6, ENST00000497488.2, ENST00000586385.5, ENST00000591534.5, ENST00000591849.5, ENST00000618469.2, ENST00000634433.2, ENST00000644379.2, ENST00000644555.2, ENST00000700182.1, ENST00000713676.1 )
WRN p.Val114Ile (p.V114I) ( ENST00000298139.7 )
PRKDC c.4413+39T>C ( ENST00000314191.7, ENST00000338368.7 )
PRKDC c.3848-634A>G ( ENST00000314191.7, ENST00000338368.7 )
PRKDC c.1623+6A>G ( ENST00000314191.7, ENST00000338368.7 )
Associated Disease
Malignant neoplasm of breast
Source Database
DisGeNET
Description
In multivariable analyses, WRN V114I (rs2230009) significantly modified the association between cumulative occupational breast dose and risk of breast cancer (adjusted for personal diagnostic exposure) (p = 0.04) and BRCA1 D652N (rs4986850), PRKDC IVS15 + 6C > T (rs1231202), PRKDC IVS34 + 39T > C (rs8178097) and PRKDC IVS31 - 634C > A (rs10109984) significantly altered the personal diagnostic radiation exposure-response relationship (adjusted for occupational dose) (p < or = 0.05).
Pubmed
17764108
Original source reporting the Gene Disease association
BeFree
DisGENET score for the Gene Disease association
0.0116396628910506
Year of publication
2008
Drugs