Annotation Detail

Information
Associated Genes
TGM1
Associated Variants
TGM1 p.Val518Met (p.V518M) ( ENST00000206765.11, ENST00000544573.5 )
TGM1 p.Val518Met (p.V518M) ( ENST00000206765.11, ENST00000544573.5 )
Associated Disease
Ichthyosiform Erythroderma, Congenital
Source Database
DisGeNET
Description
These studies extend our prior work on TGM1-deficient LI to the full spectrum of TGM1-deficient patients, showing that the CIE phenotype, when attributable to a V518M heterozygous mutation in TGM1 in combination with an inactive allele, confers a cross-linking deficiency in a variety of keratinizing epithelia, as previously shown for TGM1-negative LI.
Pubmed
16133457
Original source reporting the Gene Disease association
BeFree
DisGENET score for the Gene Disease association
0.00554838957344497
Year of publication
2005
Drugs