Annotation Detail

Information
Associated Genes
MEFV
Associated Variants
MEFV p.His478Tyr (p.H478Y) ( ENST00000541159.5, ENST00000219596.6, ENST00000339854.8, ENST00000536379.5 )
MEFV p.His478Tyr (p.H478Y) ( ENST00000219596.6, ENST00000339854.8, ENST00000536379.5, ENST00000541159.5 )
Associated Disease
Hereditary Autoinflammatory Diseases
Source Database
DisGeNET
Description
We conclude that the new H478Y MEFV mutation is the dominant pathological variant causing the inflammatory periodic syndrome in this kindred and that full-length analyses of the MEFV gene are needed to obtain an adequate diagnosis of patients with clinical suspicion of a hereditary periodic fever syndrome, especially those from non-ancestral populations.
Pubmed
14679589
Original source reporting the Gene Disease association
BeFree
DisGENET score for the Gene Disease association
0.00399568321108385
Year of publication
2004
Drugs