Annotation Detail

Information
Associated Genes
GLB1
Associated Variants
GLB1 p.Gly123Arg (p.G123R) ( ENST00000399402.7, ENST00000307377.12, ENST00000307363.10 )
GLB1 p.Gly123Arg (p.G123R) ( ENST00000307363.10, ENST00000307377.12, ENST00000399402.7 )
Associated Disease
Gangliosidosis, Generalized GM1, Type 1 (disorder)
Source Database
DisGeNET
Description
The patient had compound heterozygous mutations of the GLB1 gene: c.13_14insA (p.L5HfsX29), which was reported in a patient with infantile GM1 gangliosidosis with the near-complete absence of enzyme activity, and c.367G>A (p.G123R), which is a novel frame-shift mutation.
Pubmed
22371915
Original source reporting the Gene Disease association
BeFree
DisGENET score for the Gene Disease association
0.361900093104562
Year of publication
2012
Drugs