Annotation Detail

Information
Associated Genes
INS
Associated Variants
INS p.Arg89Leu (p.R89L), INS-IGF2 c.187+866G>T ( ENST00000512523.1, ENST00000381330.5, ENST00000397270.1, ENST00000397262.5, ENST00000250971.7 )
INS p.Arg89Pro (p.R89P), INS-IGF2 c.187+866G>C ( ENST00000397270.1, ENST00000381330.5, ENST00000397262.5, ENST00000250971.7, ENST00000512523.1 )
INS p.Arg89His (p.R89H), INS-IGF2 c.187+866G>A ( ENST00000397270.1, ENST00000381330.5, ENST00000397262.5, ENST00000250971.7, ENST00000512523.1 )
INS p.Arg89Leu (p.R89L), INS-IGF2 c.187+866G>T ( ENST00000250971.7, ENST00000381330.5, ENST00000397262.5, ENST00000512523.1, ENST00000397270.1 )
INS p.Arg89Pro (p.R89P), INS-IGF2 c.187+866G>C ( ENST00000250971.7, ENST00000381330.5, ENST00000397262.5, ENST00000512523.1, ENST00000397270.1 )
INS p.Arg89His (p.R89H), INS-IGF2 c.187+866G>A ( ENST00000250971.7, ENST00000381330.5, ENST00000397262.5, ENST00000512523.1, ENST00000397270.1 )
Associated Disease
Hyperproinsulinemia
Source Database
DisGeNET
Description
Two unrelated patients with familial hyperproinsulinemia due to a mutation substituting histidine for arginine at position 65 in the proinsulin molecule: identification of the mutation by direct sequencing of genomic deoxyribonucleic acid amplified by polymerase chain reaction.
Pubmed
2196279
Original source reporting the Gene Disease association
UNIPROT
DisGENET score for the Gene Disease association
0.122985860592883
Year of publication
1990
Drugs