Annotation Detail

Information
Associated Genes
LMNA
Associated Variants
LMNA p.Arg28Gly (p.R28G) ( ENST00000368299.7, ENST00000361308.9, ENST00000676385.2, ENST00000368300.9, ENST00000682650.1, ENST00000675939.1, ENST00000675667.1, ENST00000677389.1, ENST00000368301.6, ENST00000683032.1 )
LMNA p.Arg28Trp (p.R28W) ( ENST00000361308.9, ENST00000368299.7, ENST00000676385.2, ENST00000368300.9, ENST00000682650.1, ENST00000677389.1, ENST00000368301.6, ENST00000675939.1, ENST00000675667.1, ENST00000683032.1 )
LMNA p.Arg60Gly (p.R60G) ( ENST00000675939.1, ENST00000675667.1, ENST00000368301.6, ENST00000677389.1, ENST00000683032.1, ENST00000368299.7, ENST00000361308.9, ENST00000368300.9, ENST00000682650.1, ENST00000676385.2 )
LMNA p.Arg60Cys (p.R60C) ( ENST00000675667.1, ENST00000675939.1, ENST00000677389.1, ENST00000368301.6, ENST00000683032.1, ENST00000361308.9, ENST00000368299.7, ENST00000676385.2, ENST00000368300.9, ENST00000682650.1 )
LMNA p.Arg62Gly (p.R62G) ( ENST00000675939.1, ENST00000675667.1, ENST00000677389.1, ENST00000368301.6, ENST00000683032.1, ENST00000361308.9, ENST00000368299.7, ENST00000676385.2, ENST00000368300.9, ENST00000682650.1 )
LMNA p.Arg28Gly (p.R28G) ( ENST00000361308.9, ENST00000368299.7, ENST00000368300.9, ENST00000368301.6, ENST00000675667.1, ENST00000675939.1, ENST00000676385.2, ENST00000677389.1, ENST00000682650.1, ENST00000683032.1 )
LMNA p.Arg28Trp (p.R28W) ( ENST00000361308.9, ENST00000368299.7, ENST00000368300.9, ENST00000368301.6, ENST00000675667.1, ENST00000675939.1, ENST00000676385.2, ENST00000677389.1, ENST00000682650.1, ENST00000683032.1 )
LMNA p.Arg60Gly (p.R60G) ( ENST00000361308.9, ENST00000368299.7, ENST00000368300.9, ENST00000368301.6, ENST00000675667.1, ENST00000675939.1, ENST00000676385.2, ENST00000677389.1, ENST00000682650.1, ENST00000683032.1 )
LMNA p.Arg60Cys (p.R60C) ( ENST00000361308.9, ENST00000368299.7, ENST00000368300.9, ENST00000368301.6, ENST00000675667.1, ENST00000675939.1, ENST00000676385.2, ENST00000677389.1, ENST00000682650.1, ENST00000683032.1 )
LMNA p.Arg62Gly (p.R62G) ( ENST00000361308.9, ENST00000368299.7, ENST00000368300.9, ENST00000368301.6, ENST00000675667.1, ENST00000675939.1, ENST00000676385.2, ENST00000677389.1, ENST00000682650.1, ENST00000683032.1 )
Associated Disease
congestive heart failure
Source Database
DisGeNET
Description
On the other hand, affected subjects from three FPLD pedigrees with heterozygous R28W, R60G and R62G LMNA mutations in the amino-terminal had associated cardiomyopathy presenting as premature onset of congestive heart failure, dilated cardiomyopathy and conduction system disturbances.
Pubmed
20041886
Original source reporting the Gene Disease association
BeFree
DisGENET score for the Gene Disease association
0.00244297684872273
Year of publication
2010
Drugs