Annotation Detail

Information
Associated Genes
SMAD4
Associated Variants
SMAD4 p.Ile500Val (p.I500V) ( ENST00000342988.8, ENST00000398417.6, ENST00000588745.5, ENST00000588860.6, ENST00000589076.6, ENST00000589941.2, ENST00000590061.2, ENST00000593223.2, ENST00000714261.1, ENST00000714264.1, ENST00000714266.1, ENST00000714268.1, ENST00000714269.1, ENST00000714270.1, ENST00000714272.1 )
SMAD4 p.Ile500Thr (p.I500T) ( ENST00000714261.1, ENST00000588860.6, ENST00000589076.6, ENST00000589941.2, ENST00000398417.6, ENST00000590061.2, ENST00000593223.2, ENST00000588745.5, ENST00000342988.8, ENST00000714264.1, ENST00000714266.1, ENST00000714268.1, ENST00000714269.1, ENST00000714270.1, ENST00000714272.1 )
SMAD4 p.Ile500Met (p.I500M) ( ENST00000342988.8, ENST00000398417.6, ENST00000588745.5, ENST00000588860.6, ENST00000589076.6, ENST00000589941.2, ENST00000590061.2, ENST00000593223.2, ENST00000714261.1, ENST00000714264.1, ENST00000714266.1, ENST00000714268.1, ENST00000714269.1, ENST00000714270.1, ENST00000714272.1 )
SMAD4 p.Ile500Val (p.I500V) ( ENST00000342988.8, ENST00000398417.6, ENST00000588745.5, ENST00000588860.6, ENST00000589076.6, ENST00000589941.2, ENST00000590061.2, ENST00000593223.2, ENST00000714261.1, ENST00000714264.1, ENST00000714266.1, ENST00000714268.1, ENST00000714269.1, ENST00000714270.1, ENST00000714272.1 )
SMAD4 p.Ile500Thr (p.I500T) ( ENST00000342988.8, ENST00000714270.1, ENST00000588860.6, ENST00000589941.2, ENST00000714272.1, ENST00000588745.5, ENST00000398417.6, ENST00000714264.1, ENST00000714266.1, ENST00000714268.1, ENST00000714269.1, ENST00000589076.6, ENST00000714261.1, ENST00000593223.2, ENST00000590061.2 )
SMAD4 p.Ile500Met (p.I500M) ( ENST00000342988.8, ENST00000398417.6, ENST00000588745.5, ENST00000588860.6, ENST00000589076.6, ENST00000589941.2, ENST00000590061.2, ENST00000593223.2, ENST00000714261.1, ENST00000714264.1, ENST00000714266.1, ENST00000714268.1, ENST00000714269.1, ENST00000714270.1, ENST00000714272.1 )
Associated Disease
Growth mental deficiency syndrome of Myhre
Source Database
DisGeNET
Description
Mutations at a single codon in Mad homology 2 domain of SMAD4 cause Myhre syndrome.
Pubmed
22158539
Original source reporting the Gene Disease association
UNIPROT
DisGENET score for the Gene Disease association
0.481900093104562
Year of publication
2012
Drugs