Annotation Detail

Information
Associated Genes
ADAMTS13
Associated Variants
ADAMTS13 p.Cys508Tyr (p.C508Y) ( ENST00000355699.7, ENST00000356589.6, ENST00000371916.5, ENST00000371929.7 )
ADAMTS13 p.Cys508Tyr (p.C508Y) ( ENST00000355699.7, ENST00000356589.6, ENST00000371916.5, ENST00000371929.7 )
Associated Disease
Congenital Thrombotic Thrombocytopenic Purpura
Source Database
DisGeNET
Description
Here, we report missense and nonsense mutations in two Japanese families with Upshaw-Schulman syndrome, congenital TTP with neonatal onset and frequent relapses.
Pubmed
12181489
Original source reporting the Gene Disease association
UNIPROT
DisGENET score for the Gene Disease association
0.453224706861814
Year of publication
2002
Drugs