Annotation Detail

Information
Associated Genes
CYP21A2
Associated Variants
CYP21A2 p.Gly292Ser (p.G292S) ( ENST00000435122.3, ENST00000644719.2 )
CYP21A2 p.Gly292Arg (p.G292R) ( ENST00000435122.3, ENST00000644719.2 )
CYP21A2 p.Arg484Gln (p.R484Q) ( ENST00000435122.3, ENST00000644719.2 )
CYP21A2 p.Arg484Pro (p.R484P) ( ENST00000435122.3, ENST00000644719.2 )
CYP21A2 p.Gly292Ser (p.G292S) ( ENST00000435122.3, ENST00000644719.2 )
CYP21A2 p.Gly292Arg (p.G292R) ( ENST00000435122.3, ENST00000644719.2 )
CYP21A2 p.Arg484Gln (p.R484Q) ( ENST00000435122.3, ENST00000644719.2 )
CYP21A2 p.Arg484Pro (p.R484P) ( ENST00000435122.3, ENST00000644719.2 )
Associated Disease
congenital adrenal hyperplasia
Source Database
DisGeNET
Description
Three mutants (deletion of E196, G291S, and R483P) of steroid 21-hydroxylase (P450c21) from patients with inherited congenital adrenal hyperplasia had reduced activity toward progesterone and 17-hydroxyprogesterone after transient expression in cultured mammalian cells.
Pubmed
9497336
Original source reporting the Gene Disease association
BeFree
DisGENET score for the Gene Disease association
0.29375669260601
Year of publication
1998
Drugs