Annotation Detail

Information
Associated Genes
LMNA
Associated Variants
LMNA p.Arg225Gln (p.R225Q) ( ENST00000368297.5, ENST00000473598.6, ENST00000683032.1, ENST00000368301.6, ENST00000677389.1, ENST00000675667.1, ENST00000368300.9, ENST00000682650.1, ENST00000676385.2, ENST00000448611.6, ENST00000361308.9, ENST00000368299.7, ENST00000675939.1, ENST00000504687.7 )
LMNA p.Arg225Gln (p.R225Q) ( ENST00000361308.9, ENST00000368297.5, ENST00000368299.7, ENST00000368300.9, ENST00000368301.6, ENST00000448611.6, ENST00000473598.6, ENST00000504687.7, ENST00000675667.1, ENST00000675939.1, ENST00000676385.2, ENST00000677389.1, ENST00000682650.1, ENST00000683032.1 )
Associated Disease
muscular dystrophy
Source Database
DisGeNET
Description
The cross-referencing of these mutations in candidate genes for muscular dystrophy showed a homozygote mutation c.G674A in exon 4 of LMNA causing a protein change R225Q in an arginine conserved from human to Xenopus tropicalis and in lamin B1.
Pubmed
22431096
Original source reporting the Gene Disease association
BeFree
DisGENET score for the Gene Disease association
0.0182263315160369
Year of publication
2012
Drugs