Annotation Detail

Information
Associated Genes
CXCR4
Associated Variants
CXCR4 p.Arg338Ter (p.R338*) ( ENST00000241393.4, ENST00000409817.1, ENST00000466288.1, ENST00000696136.1, ENST00000696137.1, ENST00000696152.1, ENST00000696228.1 )
CXCR4 p.Arg338Ter (p.R338*) ( ENST00000241393.4, ENST00000409817.1, ENST00000466288.1, ENST00000696136.1, ENST00000696137.1, ENST00000696152.1, ENST00000696228.1 )
Associated Disease
WHIM syndrome
Source Database
DisGeNET
Description
A nonsense mutation (C-->T) truncating the CXC chemokine receptor 4 (CXCR4) C-terminal cytoplasmic tail domain occurred at nucleotide position 1000(R334X) of the CXCR4 gene in one allele of the patient was identified, and the person was diagnosed as having WHIM syndrome.
Pubmed
19476565
Original source reporting the Gene Disease association
BeFree
DisGENET score for the Gene Disease association
0.449771907394891
Year of publication
2009
Drugs