Annotation Detail

Information
Associated Genes
ABCC8
Associated Variants
ABCC8 MUTATION
ABCC8 MUTATION
ABCC8 p.Leu225Pro (p.L225P) ( ENST00000302539.9, ENST00000644772.1, ENST00000646902.1, ENST00000643260.1, ENST00000684571.1, ENST00000389817.8, ENST00000683136.1, ENST00000647015.1, ENST00000642271.1 )
ABCC8 p.Leu225Pro (p.L225P) ( ENST00000302539.9, ENST00000389817.8, ENST00000642271.1, ENST00000643260.1, ENST00000644772.1, ENST00000646902.1, ENST00000647015.1, ENST00000683136.1, ENST00000684571.1 )
Associated Disease
DIABETES MELLITUS, PERMANENT NEONATAL
Source Database
DisGeNET
Description
A mutation in the TMD0-L0 region of sulfonylurea receptor-1 (L225P) causes permanent neonatal diabetes mellitus (PNDM).
Pubmed
17317760
Original source reporting the Gene Disease association
BeFree
DisGENET score for the Gene Disease association
0.483800186209124
Year of publication
2007
Drugs